Phase 1/2 study
Investigational medicine, ION582 is administered by IT injection
Active, Not Recruiting
ION582 is an investigational antisense oligonucleotides (ASO) designed to increase production of UBE3A protein.
Following a screening period of up to 4 weeks, eligible participants will receive ION582. Participants will be followed for up to 32 weeks after dosing.
Participant Requirements
Inclusion Criteria
- Diagnosis of Angelman syndrome (mutation or deletion)
- Between 2 and 50 years old
- Currently receiving stable doses of anti-epileptic medication, behavioral management medications, sleep medications, gabapentin, cannabidiol, and including special diets, supplements or nutritional support for at least 3 months prior to first dose.
- Parent must be willing to not share personal or study information on social media or websites until notified that the study is completed.
Locations & Contacts
Boston Children’s Hospital
Boston, MA
Monica Ciaffi – Monica.Ciaffi@childrens.harvard.edu
Monica Ciaffi – Monica.Ciaffi@childrens.harvard.edu
University of North Carolina at Chapel Hill
Carrborro, NC
Carrborro, NC
Hannah Riehl – hannah.riehl@cidd.unc.edu
Sydney Children’s Hospital, Kids Cancer Centre
Randwick, Australia
Sheba Medical Center
Ramat Gan, Israel
Azienda Ospedaliera Universitaria Pisana
Pisa, Italy
STRONG Group University of Oxford
Oxford, Oxfordshire, United Kingdom